Аннотация
Врожденные пороки сердца (ВПС) являются одними из самых частых жизнеугрожающих врожденных заболеваний. Однако прогноз при таких заболеваниях может быть еще серьезнее при наличии экстракардиальных патологий, среди которых особенно часто с ВПС сочетаются врожденные пороки развития (ВПР) желудочно-кишечного тракта (ЖКТ). Подобное сочетание заболеваний требует быстрого и верного принятия решения в отношении хирургического лечения в первые дни жизни ребенка. Даже в изолированном виде эти заболевания могут стать показанием для экстренного или срочного хирургического вмешательства с применением этапного или первично-радикального подходов. Однако на сегодняшний день не существует универсального алгоритма лечения пациентов с подобным сочетанием врожденных заболеваний. В данной работе продемонстрированы клинические особенности сочетания ВПС и ВПР ЖКТ, которые обусловливают необходимость формирования оптимальных диагностических и лечебных алгоритмов для этой непростой группы пациентов.
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Об авторах
- Япринцев Валерий Олегович, сердечно-сосудистый хирург, мл. науч. сотр.; ORCID
- Яцык Сергей Павлович, д-р мед. наук, профессор, чл.-корр. РАН, директор Института детской хирургии; ORCID
- Мовсесян Рубен Рудольфович, д-р мед. наук, профессор, чл.-корр. РАН, заведующий отделением; ORCID
