Abstract
The combination of Ebstein’s anomaly with a ventricular septal defect (VSD) is an extremely rare case. It is believed that the co-existing VSD is favorable for the hemodynamics of the defect for several reasons. Firstly, the blood flow through the defect enters directly into the pulmonary artery instead of the antegrade pulmonary blood flow from the hypoplasized right ventricle. Secondly, the blood flow through the VSD into the right ventricle will create pressure and volume overload at the right ventricle outflow tract, which can contribute to the growth of the right ventricle. Thus, the anatomy of the Ebstein’s anomaly in combination with the defect of the interventricular septum can allow radical correction of the defect at an earlier time and give good results of surgical correction.
The article describes a case of successful cone reconstruction of Ebstein’s anomaly in combination with ventricular septal defect in a child of 1 year and 3 months.
References
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About the authors
- Viktoriya P. Doktorova, Junior Researcher; ORCID
- Aleksey I. Kim, Dr. Med. Sci., Professor, Head of Department of Cardiac Surgery for Newborns and Infants; ORCID
- Tatyana V. Rogova, Dr. Med. Sci., Leading Researcher, Head of Department of Reconstructive Surgery for Newborns and Children of the First Year of Life with Congenital Heart Disease; ORCID
- Pyatimat R. Evloeva, Junior Researcher; ORCID
- Murat O. Ediev, Junior Researcher; ORCID
- Rasul M. Kurganov, Junior Researcher; ORCID
