Abstract
The article describes a case of successful treatment of a 5-month-old patient with an extremely rare disease – a double-chambered
left ventricle with complex congenital heart disease. The pathology manifested by severe heart failure. Double-chambered left ventricle
was detected by echocardiography, confirmed by computed tomography and angiocardiography. In the left ventricle a muscular
cord is visualized, extending from the apical segments almost parallel to the interventricular septum, which divides the cavity
of the left ventricle into two chambers. There is ventricular septal defect and based on the presence of signs of early development of pulmonary hypertension, a decision was made on the need to perform a pulmonary artery banding. The patient was discharged
10 days after surgery. Given that in the literature there are not enough review articles to determine the surgical approach, we present
a discussion of disease prognosis, tactics and treatment.
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About the authors
- Tat'yana V. Rogova, Dr. Med. Sc., Leading Researcher, orcid.org/0000-0002-7610-1743;
-
Aleksey I. Kim, Dr. Med. Sc., Professor, Head of Department, orcid.org/0000-0002-1759-9895;
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Andrey V. Sobolev, Cand. Med. Sc., Leading Researcher, Endovascular Diagnosis and Treatment Physician, orcid.org 0000-0002-0186-8165;
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Svetlana A. Aleksandrova, Cand. Med. Sc., Radiologist, Senior Researcher, orcid.org/0000-0002-7795-9709;
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Elena V. Kholmanskaya, Functional Diagnostician, orcid.org/0000-0002-7384-8040;
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Tigran R. Grigor'yants, Cand. Med. Sc., Senior Researcher, orcid.org/0000-0001-9344-2593
