Abstract
Pulmonary atresia with intact ventricular septum is a critical congenital heart disease with ductus–dependent pulmonary circulation. This defect is diagnosed in the first days or months of the child’s life and has severe clinical manifestations from the moment of patient’s birth. We present a case of successful hybrid surgery in a newborn baby with type 1 pulmonary atresia with intact ventricular septum. The surgical treatment was performed in operation room with mobile angiography unit using median sternotomy approach and direct high-pressure balloon dilatation of pulmonary valve via right ventricular free wall.
References
- Schneider A.W., Blom N.A., Bruggemans E.F., Hazekamp M.G. More than 25 years of experience in managing pulmonary atresia with intact ventricular septum. Ann. Thorac. Surg. 2014; 98: 1680–6. DOI: 10.1016/J.ATHORACSUR.2014.05.085
- Крутов А.О. Хирургическое лечение новорожденных и детей первого года жизни с атрезией легочной артерии и интактной межжелудочковой перегородкой: дис. ... канд. мед. наук. М.; 2004. [Krutov A.O. Surgical treatment newborns and children of the first year of life with pulmonary atresia with intact ventricular septum. Cand. Med. Sc. Diss. Moscow; 2004 (in Russ.)].
- Hasan B.S., Bautista-Hernandez V., McElhinney D.B., Salvin J., Laussen P.C., Prakash A. et al. Outcomes of tran scatheter approach for initial treatment of pulmonary atresia with intact ventricular septum. Catheter. Cardiovasc. Interv. 2013; 81: 111–8. DOI: 10.1002/ccd.24288
- Hirata Y., Chen J.M., Quaegebeur J.M., Hellenbrand W.E., Mosca R.S. Pulmonary atresia with intact ventricular septum: limitations of catheter-based intervention. Ann. Thorac. Surg. 2007; 84: 574–80. DOI: 10.1016/j.athoracsur.2007.04.003
- Dyamenahalli U.M.B., McDonald C., Trivedi K.R., Smallhorn J.F., Benson L.N., Coles J. et al. Pulmonary atresia with intact ventricular septum: management of, and outcomes for, a cohort of 210 consecutive patients. Cardiol. Young. 2004; 14: 299–308. DOI: 10.1017/s1047951104003087
- Hanley F.L., Sade R.M., Blackstone E.H., Kirklin J.W., Freedom R.M., Nanda N.C. Outcomes in neonatal pulmonary atresia with intact ventricular septum. A multi-institutional study. J. Thorac. Cardiovasc. Surg. 1993; 105 (3): 406–27. DOI: 10.1016/S0022-5223(19)34223-0
- Guleserian K.J., Armsby L.B., Thiagarajan R.R., del Nido P.J., Mayer J.E. Natural history of pulmonary atresia with intact ventricular septum and right-ventricle-dependent coronary circulation managed by the single-ventricle approach. Ann. Thorac. Surg. 2006; 81 (6): 2250–8. DOI: 10.1016/ j.athoracsur.2005.11.041
About the authors
- Sergey A. Kotov, Cand. Med. Sc., Senior Researcher, orcid.org/0000-0003-4570-4854;
- Andrey V. Sobolev, Cand. Med. Sc., Leading Researcher, orcid.org/0000-0002-0186-8165;
- Aleksandr A. Chvamaniya, Researcher, orcid.org/0000-0002-8011-4993;
- Yuliya V. Butrim, Junior Researcher, orcid.org/0000-0001-7761-3424;
