Abstract
We present an unusual variant of partial atrioventricular septal defect with double outlet left atrium (DO LA). Diagnosis was established during a routine examination a 10-year-old child involved in sports using two-dimensional echocardiography and confirmed using magnetic resonance imaging. The separate communications between the left atrium, the left ventricle and the right ventricle was diagnosed in combination with small atrial septal defect of ostium primum type and the trileaflet left atrioventricular valve, in absence of obstruction and any significant valve insufficiency. An absence of clinical symptoms, indications for therapeutic and surgical treatment have not been established. This observation complements the previous publications of DO LA, where this anomaly was an element of complex cardiac heart defects, and also illustrates the exceptional anatomical variability of the open atrioventricular septal defect.
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About the authors
- Yuriy Yu. Kornoukhov, Pediatric Cardiologist, orcid.org/0000-0002-4775-8543
- Mariya V. Il’ina, Pediatric Cardiologist, orcid.org/0000-0002-6930-9343
- Mariya M. Belyaeva, Pediatric Cardiologist, orcid.org/0000-0002-1369-7754
- Valeriy V. Khovrin, Dr. Med. Sc., Chief Researcher, orcid.org/0000-0002-6720-4126
- Vladimir N. Il’in, Dr. Med. Sc., Professor, Cardiovascular Surgeon, Head of Department, orcid.org/0000-0003-4162-068X
