Abstract
Double-outlet right ventricle (DORV) is a complex congenital heart malformation in which greater parts of the arterial trunks arise from right ventricle. Probably DORV is the most sophisticated congenital heart defect due to the wide spectrum of its anatomical variations caused by different types of ventricular septal defects and relationships of the arterial trunks. Knowledge of precise anatomy of the pathology is a key for understanding conotrucal anomalies as well as proper orientation in intracardiac structures during an operation. The modern morphological viewpoint on DORV along with anatomical description of different types of the anomaly based on autopsied specimens have been described in this article.
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About the authors
- Konstantin V. Shatalov, Dr. Med. Sc., Professor, Head of Department, ORCID
- Konstantine M. Dzhidzhikhiya, Cand. Med. Sc., Cardiac Surgeon,
ORCID
- Margarita V. Gordeeva, Cand. Med. Sc., Senior Researcher, Pathologist,
ORCID