Abstract
Maldevelopment and disorientation of the conal septum during fetal development leads to formation of conotruncal anomalies. Thus,
tetralogy of Fallot, double-outlet right ventricle (DORV) and transposition of great arteries are caused by false orientation of the conal
septum, severity of which may vary from one malformation to another. Thereby these anomalies are considered to be the result of
the same pathological process. In the spectrum of conotruncal anomalies DORV occupies middle position, wherein the clear anatomical borders between them are absent. In this article the modern viewpoint on anatomically transitional forms between DORV and
tetralogy Fallot, on one hand, and DORV and transposition, on the other hand, has been discussed.
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About the authors
- Konstantin V. Shatalov, Dr. Med. Sc., Professor, Head of Department, ORCID
- Konstantine M. Dzhidzhikhiya, Cand. Med. Sc., Cardiac Surgeon, ORCID
- Margarita V. Gordeeva, Cand. Med. Sc., Senior Researcher, Pathologist, ORCID
