Abstract
The frequency of unilateral absence of the pulmonary artery is 1:200,000–300,000 in the general population, while in 56.5% of cases it
has been associated with congenital heart defects, in particular with tetralogy of Fallot. In such cases, replacement of an absent pulmonary
artery is necessary. Surgical methods of the unilateral absent pulmonary artery replacement using PTFE or Dacron tube, autologous pericardium,
homograft patch, using native pulmonary artery tissue, direct end to end anastomosis have described. This article represents our
first experience of the new method of replacement of the absent proximal part of the left pulmonary artery with the autologous pericardium
and xenopericardial monocusp patch.
References
- Angeborener F.O. Defect der rechten lungenarterie. Virchows
Arch. Pathol. Anat. 1868; 43: 420.
- Bouros D., Pare P., Panagou P., Tsintiris K., Siafakas N. The
varied manifestation of pulmonary artery agenesis in adulthood.
Chest. 1995; 108: 670–6.
- Kadir I., Thekudan J., Dheodar A., Jones M., Carroll K.
Congenital unilateral pulmonary artery agenesis and
aspergilloma. Ann. Thorac. Surg. 2002; 74: 2169–71.
- Bockeria L., Makhachev O., Khiriev T., Abramyan M.
Congenital isolated unilateral absence of pulmonary artery and
variants of collateral blood supply of the ipsilateral lung.
Interact. Cardiovasc. Thorac. Surg. 2011; 12: 509–10.
- Kobayashi J., Hirose H., Matsuda H., Nakano S., Ihara K.,
Kawashima Y. Surgical treatment of tetralogy of Fallot with a
congenitally absent left pulmonary artery. Nippon Kyobu
Geka Gakkai Zasshi. 1985; 33: 1101–6.
- Juca E., Carvalho W., Jr., de Oliveira F., Araujo J.,
Mont’Alverne R., Paes J., Jr. et al. Surgical treatment of tetralogy
of Fallot with left pulmonary artery agenesis: report of
2 cases. Arq. Bras. Cardiol. 1982; 38: 39–43.
- Murphy D., Winlaw D., Cooper S., Nunn G. Successful early
surgical recruitment of the congenital disconnected pulmonary
artery. Ann. Thorac. Surg. 2004; 77: 29–35.
- Шаталов К.В., Джиджихия К.М., Бакулева Н.П., Зайцев Л.В.
Моностворчатый протез клапана легочной артерии. Патент
РФ, № 175106; 2017 / Shatalov K.V., Dzhidzhikhiya K.M.,
Bakuleva N.P., Zaytsev L.V. Pulmonary valve monocusp prosthetic.
Patent RF, № 175106, 2017 (in Russ.).
- Presbitero P., Bull C., Haworth S., Leval M. Absent or occult
pulmonary artery. Brit. Heart J. 1984; 52: 178–85.
- Sreeram N., Asante-Korang A., Ladusans E. Distal ductal origin
of the right pulmonary artery: prospective diagnosis and
primary repair in infancy. Int. J. Cardiol. 1992; 35: 272–4.
- Moreno-Cabral R., McNamara J., Reddy J., Caldwell P.
Unilateral absent pulmonary artery: surgical repair with a new
technique. J. Thorac. Cardiovasc. Surg. 1991; 3: 463–5.
- Welch K., Hanley F., Johnston T., Cailies C., Shah M. Isolated
unilateral absence of right proximal pulmonary artery: surgical
repair and follow up. Ann. Thorac. Surg. 2005; 79: 1399–402.
- Kosaka Y., Kurosawa H., Hishino S., Shin’oka T., Isomatsu Y.,
Tsuji Y. Surgery for unilateral absence of pulmonary artery
using autologous tissue. Ann. Thorac. Surg. 2003; 76: 1281–3.
- Green G., Reppert E., Cohlan S., Spencer F. Surgical correction
of absence of proximal segment of left pulmonary artery.
Circulation. 1968; 37: 62–9.
- Бокерия Л.А., Махачев О.М., Беришвили Д.О., Хириев Т.Х.,
Адкин Д.В., Крупянко С.М. и др. Врожденное одностороннее отсутствие легочной артерии: хирургическое восстановление антеградного кровотока в ипсилательном легком.
Детские болезни сердца и сосудов. 2011; 3: 47–53 /
Bockeria L.A., Makhachev O.M., Berishvili D.O., Khiriev
T.Kh., Adkin D.V., Krupyanko S.M. et al. Congenital unilateral
anbense of the pulmonary artery: Врожденное односто-
роннее отсутствие легочной артерии: surgical restoration of
antegrade blood flow in the ipsilating lung. Children’s Heart
and Vascular Diseases. 2011; 3: 47–53.
About the authors
- Konstantin V. Shatalov, Dr Med. Sc., Professor, Head of Department;
- Konstantine M. Dzhidzhikhiya, Cand. Med. Sc., Cardiovascular Surgeon, orcid.org/0000-0003-3040-6901
