Abstract
Scimitar syndrome is a congenital heart disease characterized by complete or partial anomalous drainage of the pulmonary veins into the systemic venous blood flow, and combined with pulmonary involvement. In the world literature, single observations of this condition have been described, and the lack of complete classification leads to errors in diagnosis and differences in terminology and description of the disease. This report describes a case of surgical treatment of a rare form of scimitar syndrome with partial anomalous drainage of right pulmonary veins into the right atrium and intact atrial septum.
References
- Çiçek S., Hulusi A.A., Ugurlucan M., Yildiz Y., Ay S. Scimitar syndrome: the curved Turkish sabre. Semin. Thorac. Cardiovasc. Surg. Pediatric Card. Surg. Annu. 2014; 17: 1.
- Najm H.K., Williams W.G., Coles J.G., Rebeyka I.M., Freedom R.M. Scimitar syndrome: twenty years’ experience and results of repair. J. Thorac. Cardiovasc. Surg. 1996; 112: 1161–1169.
- Graham G., Dearani J.A., Mathew J., Miranda W.R., King K.S., Schaff H.V. et al. Partial anomalous pulmonary venous connection with intact atrial septum: early and midterm outcomes. Ann. Thorac. Surg. 2023; 115 (6): 1479–1484. DOI: 10.1016/j.athoracsur.2022.04.031
- Demir E., Aşkın M., Midyat L., Gülen F., Ülger Z., Tanaç R. et al. Scimitar syndrome associated with partial anomalous pulmonary venous draining into superior vena cava. Eur. J. Pediatr. 2010; 169: 1263–1265.
- Kim S.J., Ann S.H., Park S. An unusual case of scimitar syndrome with drainage to the right atrium. J. Cardiovasc. Imag. 2022; 30 (3): 222–225. DOI: 10.4250/jcvi.2021.0184
- Najm H.K., Williams W.G., Coles J.G., Rebeyka I.M., Freedom R.M. Scimitar syndrome: twenty years' experience and results of repair. J. Thorac. Cardiovasc. Surg. 1996; 112 (5): 1161–1169. DOI: 10.1016/S0022-5223(96)70129-0
- Shikhieva L.S., Abdullaev F.Z., Bagirov I.M., Mirzai A.I., Rustamova Ya.K., Akhmedov T.M. Morfology and management options of anomalous right pulmonary venous return in to the inferior vena cava in adults. Grudnaya i Serdechno-Sosudistaya Khirurgiya. 2023; 65 (4): 493–501 (in Russ.). DOI: 10.24022/0236-2791-2023-65-4-493-501
- Kim A.I., Rogova T.V., Tiofeeva O.Yu. Correction of rare mixed total anomalous pulmonary venous connection. Children’s Heart and Vascular Diseases. 2021; 18 (4): 306–308 (in Russ.). DOI: 10.24022/1810-0686-2021-18-4-306-308
- Healey J.E. An anatomic survey of anomalous pulmonary veins: their clinical significance. J. Thorac. Cardiovasc. Surg. 1952; 23 (5): 433–444. PMID: 18036929.
- Volkov S.S., Zelenikin M.A. Risk in pediatric congenital heart surgery in children. Part 2. Postoperative complications. Grudnaya i Serdechno- Sosudistaya Khirurgiya. 2022; 64 (2): 131–136 (in Russ.). DOI: 10.24022/0236-2791-2022-64-2-131-136
- Fragata J., Magalhães M., Baquero L., Trigo C., Pinto F., Fragata I. Partial anomalous pulmonary venous connections: surgical management. W. J. Pediatr. Congen. Heart Surg. 2013; 4 (1): 44–49.
- Kahrom M., Kahrom H. Scimitar syndrome and evolution of managements. Pan Afr. Med. J. 2009; 3: 20.
About the authors
- Konstantin V. Shatalov, Dr. Med. Sci., Professor, Deputy Director for Scientific Work, Head of Department of Emergency Surgery of Congenital Heart Disease; ORCID
- Irina V. Arnautova, Dr. Med. Sci., Chief Researcher, Cardiovascular Surgeon; ORCID
- Sergey V. Patsera, Resident Physician; ORCID
- Konstantine M. Dzhidzhikhiya, Dr. Med. Sci., Head of Laboratory of Allogenic Materials for Cardiovascular Surgery, Cardiovascular Surgeon; ORCID
- Artur M. Gamisoniya, Cand. Med. Sci., Cardiovascular Surgeon; ORCID
