Детские болезни сердца и сосудов


Детские болезни сердца и сосудов


Children's Heart and Vascular Diseases

Children's Heart and Vascular Diseases. 2024, 21 (4)

Title page, pdf
Contents, pdf
About journal, pdf

Reviews

Myocardial dysfunction in progressive Duchenne/Becker muscular dystrophy: current treatment methods
Rozhkova A.B.1, Groznova O.S.1 2 4, Kovalev I.A.31
1 Veltischev Research and Clinical Institute for Pediatrics and Pediatric Surgery, Pirogov Russian National Research Medical University, Moscow, Russian Federation
2 Pirogov Russian National Research Medical University, Moscow, Russian Federation
3 Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation
4 Charity Fund for Medical and Social Genetic Aid Projects “Life Genome”, Moscow, Russian Federation

Original articles

Genophenotypic risk factors for atherosclerotic vascular disease in children with heterozygous familial hypercholesterolemia
Sadykova D.I.1 2, Khaliullina Ch.D.1 1, Galimova L.F.1 2, Slastnikova E.S.1 2 3, Shagimardanova E.I.2, Shigapova L.Kh.2, Salakhova K.R.1 2
1 Kazan State Medical University, Kazan, Russian Federation
2 Kazan (Volga Region) Federal University, Kazan, Russian Federation
3 Children’s Republican Clinical Hospital, Kazan, Russian Federation

Risk factors for the development of tachycardia-induced cardiomyopathy in children with idiopatic ventricular arrhythmia
Chueva K.A., Kofeynikova O.A., Tatarskiy R.B., Lebedev D.S., Pervunina T.M., Vasichkina E.S.
Almazov National Medical Research Centre, St. Petersburg, Russian Federation

Features of the clinical course of hupertrophic cardiomyopathy in children with onset in the first year of life against the background of mutations in sarcomeric and RAS-associated genes
Fetisova S.G., Melnik O.V., Sitnikova K.A., Fomicheva Yu.V., Sokolnikova P.S., Vershinina T.L., Fedorova O.V., Pervunina T.M., Kostareva A.A., Vasichkina E.S.
Almazov National Medical Research Centre, St. Petersburg, Russian Federation

Clinical and genetic characteristics of pediatric restrictive cardiomyopathy caused by pathogenic variants in the TNNI3 gene
Sdvigova N.A., Basargina E.N., Zharova O.P., Gandaeva L.A., Basargina E.Yu., Silnova I.V., Pushkov A.A., Savostyanov K.V.
1 National Medical Research Center for Children's Health, Moscow, Russian Federation
2 Filatov Clinical Institute of Child Health, Sechenov First Moscow State Medical University, Moscow, Russian Federation

Structural changes in the myocardium in patients with catecholaminergic polymorphic ventricular tachycardia
Kulbachinskaya E.K., Bereznitskaya V.V., Terekhova N.V., Kovalev I.A.
1 Research Clinical Institute of Pediatrics and Pediatric Surgery named after Academician Yu.E. Veltishchev, Russian National Research Medical University named after N.I. Pirogov, Moscow, Russian Federation
2 Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation

Echocardiographic characteristics of the right heart in young patients with ventricular pacing in the long postoperative period
Garipov A.S., Pateyuk I.V., Drozdovskiy K.V.
1 Republican Scientific and Practical Center of Pediatric Surgery, Minsk, Republic of Belarus
2 Belarusian State Medical University, Minsk, Republic of Belarus

Case reports

QRS alternans in the long QT syndrome – a new sign of dangerous arrhythmias?
Makarov L.M., Komolyatova V.N., Zaklyazminskaya E.V., Besportochnyy D.A., Islanov I.О., Kiseleva I.I.
1 Federal Scientific and Clinical Center for Children and Adolescents, Moscow, Russian Federation
2 Russian Scientific Center of Surgery named after Academician B.V. Petrovsky, Moscow, Russian Federation

Chief Editor

Konstantin V. Shatalov
MD, PhD, DSc, Professor
Bakoulev National Medical Research Center for Cardiovascular Surgery


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