Abstract
Anomalous origin of branch pulmonary artery from the ascending aorta (AOLA) (hemitruncus) is an extremely rare congenital heart disease (CHD). The overall incidence is 0.1–0.33% among all congenital heart diseases. To date, less than 150 cases of anomalous origin of a pulmonary artery from the ascending aorta have been registered in the world. 95% of patients were under one year old and the vast majority underwent surgical correction of the defect. The survival rate of patients without surgical after repair 1 year of life is approximately 20%. The clinical picture of CHD with hypervolemia of the small circulatory circle can be “masked” as lung diseases. In the article, we presented a case of late diagnosis of abnormal divergence of the right pulmonary artery from the ascending aorta in a 24-year-old man.
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About the authors
- Ekaterina E. Varakina, Resident Doctor; ORCID
- Irina Yu. Baryshnikova, Cand. Med. Sci., Associate Professor; ORCID
- Anna M. Vaneeva, Ultrasound Diagnostics Doctor, Junior Researcher; ORCID
- Ruslan A. Aybazov, Cardiovascular Surgeon; ORCID
- Marina Yu. Mironenko, Cand. Med. Sci., Ultrasound Diagnostics Doctor, Head of the Ultrasound Diagnostics Department; ORCID
