Abstract
Pulmonary arteriovenous malformations (PAVM) are a developmental defect consisting in the presence of an abnormal arteriovenous anastomosis at various levels of the division of pulmonary vessels and leading to intrapulmonary shunting of blood from right to left. Most often, this defect is a manifestation of hereditary hemorrhagic telangiectasia and is clinically characterized by the development of nosebleeds, shortness of breath and cyanosis. Despite the fact that the vessels formed as a result of angiogenesis do not have a tendency to become malignant, their presence predisposes the patient to the development of pulmonary hypertension, paradoxical embolism, including ischemic stroke and brain abscess, which requires timely diagnosis and treatment of the pathology. The clinical case presented in this article is an example of the complexity of diagnosing PAVM that has been asymptomatic for a long time and the difficulty of its differential diagnosis with other diseases of the cardiovascular and respiratory systems in children. The alertness of the primary care physician in the presented clinical case made it possible to detect LAVM in a child in a timely manner, before the development of severe complications, and successfully carry out its transcatheter embolization using the Amplatzer Vascular Plug II device.
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About the authors
- Artem V. Gorbatykh, Cand. Med. Sci., Head of Research Laboratory of Interventional Surgery, Endovascular Surgeon; ORCID
- Denis A. Manannikov, Endovascular Surgeon; ORCID
- Ilya A. Soynov, Cand. Med. Sci., Cardiovascular Surgeon; ORCID
- Aleksey A. Prokhorikhin, Cand. Med. Sci., Endovascular Surgeon; ORCID
- Dmitriy D. Zubarev, Cand. Med. Sci., Head of Department of X-ray Surgical Methods of Diagnosis and Treatment; ORCID
- Igor I. Averkin, Pediatric Cardiologist; ORCID
- Alina A. Ivanilova, Resident Physician; ORCID
- Mikhail A. Chernyavskiy, Dr. Med. Sci., Chief Researcher, Head of Department of Vascular and Interventional Surgery, Cardiovascular Surgeon; ORCID
