Successful performance of the Bentall–De Bono procedure in a child with critical aortic valve stenosis and obstruction of the aortic arch

Authors: Podoksenov A.Yu., Kotov S.A., Gorban D.A., Tumanyan M.R., Makarenko M.V., Makhalin M.V.

Company: Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation

Cite as: Podoksenov A.Yu., Kotov S.A., Gorban D.A., Tumanyan M.R., Makarenko M.V., Makhalin M.V. Successful implementation of the Bentall–De Bono operation in a child with critical aortic valve stenosis and obstruction of the aortic arch. Children’s Heart and Vascular Diseases. 2026; 23 (1): 39–48 (in Russ.). DOI: 10.24022/1810-0686-2026-23-1-39-48

Received / Accepted: 18.06.2025 / 14.01.2026

Keywords: aortic root replacement in children aortic arch repair Bentall-De Bono operation in children aortic valve stenosis systemic blood flow obstruction in children obstruction of the aortic arch

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Abstract

Congenital heart defects with systemic blood flow obstruction are often accompanied by a severe clinical condition, especially in the neonatal period. One of such defects is critical aortic valve stenosis. Performing radical correction of the defect in a newborn child is associated with high risks of life-threatening complications. In some cases, the operation of choice is hemodynamic correction to stabilize the clinical condition in the form of narrowing of the pulmonary artery branches and stenting of the patent ductus arteriosus.

We present a clinical case of successful staged surgical treatment of a child with critical aortic stenosis in combination with hypoplasia of the aortic arch and multiple defects of the interventricular septum. On the 9th day of life, bilateral narrowing and stenting of the patent ductus arteriosus were performed. At the age of 5 months, the child successfully underwent radical correction of the defect: Bentall–De Bono operation with prosthetics of the aortic arch and plastic surgery of the interventricular septal defect.

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About the authors

Andrey Yu. Podoksenov, Cand. Med. Sci., Cardiovascular Surgeon; ORCID
Sergey A. Kotov, Cand. Med. Sci., Cardiovascular Surgeon; ORCID
Diana A. Gorban, Postgraduate, Cardiovascular Surgeon; ORCID
Margarita R. Tumanyan, Dr. Med. Sci., Professor, Head of the Department of Intensive Cardiology of Premature and Infants with CHD; ORCID
Maria V. Makarenko, Pediatric Cardiologist; ORCID
Maxim V. Makhalin, Cand. Med. Sci., Cardiovascular Surgeon; ORCID

Chief Editor

Konstantin V. Shatalov
MD, PhD, DSc, Professor
Bakoulev National Medical Research Center for Cardiovascular Surgery

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