Abstract
Residual interventricular defects, mitral valve insufficiency, residual right ventricular outflow tract and other postoperative
complications after radical correction of complete form of atrioventricular canal combined with Fallot's
tetralogy are associated with reoperations which increase the risk of unfavorable outcome. The questions of terms
for performing radical correction, necessity of primary palliative interventions and surgical technique are under discussion.
Objective: to analyze the results of treatment of patients with this pathology in cardiosurgical department of Saint-
Petersburg City Children's Hospital.
Material and methods: All patients underwent closure of septal defects with two-patch technique (ventricular
septal defect was closed with a xenopericardial patch in a form of comma). Mitral valve plasty consisted of
suturing the cleavage of anterior leaflet with separate sutures. VSD was closed using transatrial approach in 7
cases and superio-anterior part of conal septum was closed using ventriculotomy in 4 cases. Right ventricular
outflow tract reconstruction was performed with different techniques and depended on anatomical features in
every case.
Results. Early postoperative period was uneventful in most cases. Mean duration of ICU-stay was 2.5 days. Mean duration
of mechanical ventilation was 21 hours. There were no lethal outcomes during in-hospital and long-term periods.
Echocardiogram on discharge showed satisfactory results of correction. The follow-up period was 2-11 years.
Conclusions. According to our successful experience we conclude that radical correction of common atrioventricular
canal with Fallot's tetralogy can be performed at earlier age. Little data don't allow us to make statistically significant
conclusions, but we consider the single-stage correction of this rare combination of congenital heart defects
to be effective method of treatment.
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