Abstract
The Taussig-Bing anomaly represents the variety of the double outlet right ventricular syndrome. Subpulmonic ventricular septal defect and
absence of stenosis of the pulmonary artery are the morphologic manifestations of the anomaly. The Taussig-Bing anomaly incidence comprises
10-30% of double outlet right ventricle syndrome.
At present the creation of a tunnel between the left ventricle and the pulmonary artery in combination with the arterial switch has been considered
as “gold standard” in surgical treatment of patients with the Taussig-Bing anomaly which should be preferably performed within the first
year of life. But the considerable number of patients has been admitted to hospital when they are much older. This category of patients can
undergo the operation of the atrial switch with both closure of the ventricular septal defect or with keeping it open i.e. palliative atrial switch. The
main factor restricting the feasibility of the defect radical correction is pulmonary hypertension that affects the immediate and long-term outcomes
of the operation. At the same time the manifested disproportion between sizes of the aorta and pulmonary artery made it hard to perform
surgery of arterial switch and in patients of 4 years old with high pulmonary hypertension can become the risk factor for unfavorable outcome.
Thus the individual approach is needed towards patients with this congenital heart defect complicated by high pulmonary hypertension. The
complex assessment of the condition of the pulmonary circulation as well as analysis of diagnosis findings before the operation allow to decide
if the patient can be operated and to choose the tactics for the defect surgical correction.
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