Abstract
This article is dedicated to history of description of complex anomalies of left side of heart, ascending aorta and aortic arch in newborns
known as "hypoplastic left heart syndrome", one of the challenging congenital heart defects for correction. First observation of
this anomaly was in 1807 by J.R. Farre. Subsequently, his compatriot E.L.R. Romberg (1828), Viennese pathologist C. von Rokitansky
(1844), group of German, Austrian and French doctors, including H.A. Bardeleben (1851), as well as English physician and
pathologist T.B. Peacock (1866) and Russian paediatrician СА. Rauchfuss (1869) specified and supplemented anatomical features
of the malformation, explained its etiology and pathogenesis, described hemodynamics and clinical manifestations. Moreover, there
were described two-, three- and four-chamber hypoplastic hearts, hearts with patent and closed foramen ovale and ventricular septal
defect (C. Heath, 1864-1865; C.A. Rauchfuss, 1869). In total, we analysed approximately 30 such descriptions made by XIX
century's doctors. Crucial in understanding of features of the anomaly, cause of origin and development are observations of J.R.Farre
(anatomy, clinical features, pathology, tanatogenesis; 1814) and СА. Rauchfuss (anatomy of spectrum of the malformation, physiology,
classification, clinical manifestations, etiology and pathogenesis; 1968). Doctors and pathologists of XX century - М. Lev
(1952), J.A. Noonan and A.S. Nadas (1958), S.N. Sinha et al. (1968) and C.I. Tchervenkov et al. (1998) expounded modern view
in anatomy, physiology and pathology of the syndrome, which underlay inventions of its surgical management.
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