Abstract
Tetralogy of Fallot with pulmonary atresia is a complex congenital heart defect. Tactics of treatment depends on the severity of
anatomic disorders and morphology of pulmonary blood flow. Two-thirds of patients have a large aorto-pulmonary collateral arteries
(APCA), patent ductus arteriosus as a source of pulmonary circulation. Rare blood supply to the lungs through the aorta-pulmonary
window, saved 5th aortic arch or fistula of the coronary arteries is rarely observed. Clinical observation demonstrates a rare source of
pulmonary blood flow – collateral vessels extending from the aortic sinuses – which helps to showcase the capacity of special methods
of diagnostics, to start the discussion on aspects of occurrence and treatment according to the literature.
References
- Myung K. Park pediatric cardiology. 4th ed. Mosby, Inc.; 2002.
- Macartney F.J., Scott O., Deverall P.B. Hemodynamic and
anatomical characteristics of pulmonary blood supply in pulmonary
atresia with ventricular septal defect – including a case of
persistent fifth aortic arch. British Heart J. 1974; 36: 1049–60.
- Барышникова И.Ю., Шарадзе Т.З., Беришвили Д.О.,
Соболев А.В. Редкий вариант анатомии аортолегочной
коллатеральной артерии у пациента с атрезией легочной
артерии с дефектом межжелудочковой перегородки I типа.
Детские болезни сердца и сосудов. 2013; 1: 59–60 /
Baryshnikova I.Yu., Sharadze T.Z., Berishvili D.O., Sobolev
A.V. The rare variant of anatomy of the aortopulmonary
collateral artery in a patient with the pulmonary artery atresia
with the ventricular septal defect of the 1st type. Detskie
bolezni serdtsa i sosudov. 2013; 1: 59–60 (in Russ.).
- Thiene G., Frescura C., Bortolotti U., del Maschio A., Valente M.
The systemic pulmonary circulation in pulmonary atresia with
ventricular septal defect: concept of reciprocal development of the
fourth and sixth aortic arches. Am. Heart J. 1981; 101: 339–44.
- Toyada Y., Yamaguchi M., Ohashi H. et al. Staged repair of
tetralogy of Fallot and pulmonary atresia without central pulmonary
arteries. Ann. Thorac. Surg. 1996, 61: 210–3.
- Чебан В.Н., Самсонов В.Б., Кокшенев И.В., Шинкарева Т.В. Случай успешной унифокализации легочного кровотока после реконструкции путей оттока из правого желудочка при атрезии легочной артерии с дефектом межжелудочковой перегородки. Детские болезни сердца и
сосудов. 2013; 1: 48–51 / Cheban V.N., Samsonov V.B.,
Kokshenev I.V., Shinkareva T.V. The case of successful unifocalisation
of the pulmonary blood flow after repair of the right
ventricular outflow tract in the condition of pulmonary artery
atresia with ventricular septal defect. Detskie bolezni serdtsa
i sosudov. 2013; 1: 48–51 (in Russ.).
- Reddy V.M., Liddicoat J.R., Hanley E.L. Midline one-stage
complete unifocalization and repair of pulmonary atresia with
ventricular septal defect and major aortopulmonary collaterals.
J. Thorac. Cardiovasc. Surg. 1995; 109: 832–45.
- Yagihara T., Yamomoto F., Nishigaki K. et al. Unifocalization
for pulmonary atresia with ventricular septal defect and major
aortopulmonary collateral arteries. J. Torac. Cardiovasc. Surg.
1996, 112: 392–402.
- Bull K., Somerville J., Spiegelhalter D. Presentation and attrition
in pulmonary atresia. J. Am. Coll. Cardiol. 1995; 25:
491–9.
- Kirklin J.W., Barratt-Boyes B.G. Cardiac Surgery. New York:
Churchill Livingstone; 1993: 942–73.
