Abstract
Surgical treatment of subaortic membrane extremely as a rare congenital heart disease (CHD) have discussed. The presence of subaortic
membrane among CHD-group remains disputable. The clinical features of the defect requires the precise dynamic monitoring due to the
aggressive growth of membrane and left ventricle outlet pressure gradient and as a consequence the development of hyperthrophy and
remodeling of the left ventricle, the insufficiency of aortic and mitral valves. Timely diagnostics and treatment help to avoid complications.
References
1. Шаталов К.В. Обструкция выхода из левого желудочка.
В кн.: Бокерия Л.А., Шаталов К.В. (ред.) Детская кардио-
хирургия: Руководство для врачей. М.: НЦССХ им. А.Н. Ба-
кулева МЗ РФ; 2016.
2. Зиньковский М.Ф. Подклапанный стеноз аорты. В кн.: Во-
зианов А.Ф., Зиньковский М.Ф. (ред.) Врожденные пороки
сердца. Киев: Книга-полюс; 2010.
3. Кривощеков Е.В., Ковалев И.А., Шипулин В.М. (ред.)
Врожденные пороки сердца: Справочник для врачей.
Томск: STT; 2009.
4. Орлов В.Е., Белоусов Ю.В. Особенности диагностики и
лечения редко встречающегося морфологического типа
субаортального стеноза – куполообразной мембраны. Со-
временные технологии в медицине. 2013; 3: 89–92.
5. Brauner R., Laks H., Drinkwater D., Shvarts O., Eghbali K.,
Galindo A. Benefits of early surgical repair in fixed subaortic
stenosis. J. Am. Call. Cardiaol. 1997; 30: 1835–42.
6. Somerville J. Fixed subaortic stenosis – a frequently misunderstood
lesion. Int. J. Cardiol. 1985; 8: 145–8.
7. Cape E.G., Vanauker M.D., Sigfusson G. et. al. Potential role of
mechanical stress in the etiology of pediatric heart disease:
septal shear stress in subaortic stenosis. J. Am. Coll. Cardiol.
1997; 30: 247–54.
8. Gewillig M., Daenen W., Dumoulin M., Van der Hauwaert L. Rheologic
genesis of discrete subvalvular aortic stenosis: a Doppler
echocardiographic study. J. Am. Coll. Cardiol. 1992; 19: 818–24.
9. Kitchiner D., Jackson M., Malajya N., Walsh K., Peart I.,
Arnold R. Incidence and prognosis of obstruction of the left
ventricular outflow tract in Liverpool (1960–91): a study of
313 patients. B. Heart J. 1994; 71 (6): 588.
10. Freedom R.M. The long and the short of it: some thought
about the fixed forms of left ventricular outflow tract obstruction.
J. Am. Coll. Cardiol. 1997; 30: 1843–6.
11. Hunter S. Congenital anomalies of the aortic valve and left ventricular
outflow tract. In: Andersen R.H., Baker E.J.,
Macartney F.J. (Eds.). Pediatric Cardiology. 2nd ed. Churchill
Livingstone; 2002: 1481–503.
12. Jonas R.A. Left ventricular outflow tract obstruction: aortic
valve stenosis, subaortic stenosis, supravalvar aortic stenosis.
In: James DiNardo J., Laussen P.C., Howe R., LaPierre R.,
Matte G. (Eds.) Comprehensive Surgical Management of
Congenital Heart Disease. CRC Press; 2014.
13. Miller D.V. Discrete membranouse subaortic stenosis. Cardiac
Valves, Native. In: Revelo M.R., Butany J., Fyfe B., Larsen B.T.,
Maleszewski J.J. (Eds.) Diagnostic cardiovascular pathology.
Lippincott Williams & Wilkins; 2014.
About the authors
- Kim Aleksey Ivanovich, Dr Med. Sc., Professor, Head of Department, orcid.org/0000-0002-1759-9895;
- Rogova Tat'yana Vladimirovna, Dr Med. Sc., Leading Researcher, Deputy Head of Department, orcid.org/0000-0002-7610-1743;
- Kurganov Rasul Murzabekovich, Junior Researcher, Cardiovascular Surgeon, orcid.org/0000-0002-5164-5576;
- Kholmanskaya Elena Vladimirovna, Ultrasonic Diagnostics Physician, orcid.org/0000-0002-7384-8040