Abstract
In this description of the clinical case, repair of the rarest pathology-the ring-sling complex in combination with a double outlet right
ventricle in a child of 3 months age old is presented. The ring-sling complex consists of complete cartilaginous rings together with an
abnormal origin of the left branch of the pulmonary artery from the right branch with a retro-tracheal its course and the formation of
a vascular loop or the so-called sling. In the world literature of this combination, including sliding tracheal plastic and radical correction
of the double outlet right ventricle has not been described yet. A feature of the presented observation is also the patient's early
age which is original for Russia at time of surgical operation. Interesting for the clinician, there are also sudden changes in the clinical
state of the patient as a result of the course of the disease, which ultimately required, in addition to reimplantation of the aberrant
left pulmonary artery, the performance of salvage tracheoplasty with the need for an extended seance of extracorporeal membrane
oxygenation procedure. It should also be noted that active cardiac surgery of patients with concomitant pathology of the trachea
under conditions of bypass circulation in our country appeared only in the last few years. In this regard, each such observation is valuable
for the accumulation of native experience which is still limited mainly as single case-reports.
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About the authors
- Bazylev Vladlen Vladlenovich, Dr Med. Sc., Professor, Chief Physician, orcid.org/0000-0001-6089-9722;
- Chernogrivov Igor' Evgen'evich, Dr Med. Sc., Cardiovascular Surgeon, orcid.org/0000-0002-6619-3875;
- Gornostaev Aleksandr Aleksandrovich, Anesthesiologist-Intensivist, Head of Department, orcid.org/0000-0002-4477-0037;
- Paramonova Tat'yana Innokent'evna, Radiologist, Head of Department;
- Suleymanov Shakhriyar Fazailovich, Anesthesiologist-Intensivist;
- Toshchev Petr Nikolaevich, Anesthesiologist-Intensivist;
- Shiganov Aleksandr Vladimirovich, Endoscopist; Chernogrivov Aleksey Evgen'evich, Dr Med. Sc., Cardiovascular Surgeon, Head of Department, orcid.org/0000-0002-6207-4799
