Abstract
Pulmonary atresia with septal defect with the double aortic arch is an extremely rare congenital heart disease. This article presents a case
of successful stage surgical treatment of pulmonary atresia with ventricular septal defect with the double aortic arch in combination with
multiple malformations, including phocomelia. In Bakoulev National Medical Research Center for Cardiovascular Surgery in department
of newborns with congenital heart disease entered the patient with pulmonary atresia with ventricular septal defect with the double aortic
arch and phocomelia.
The patient was examined and had undergone surgical treatment. Well-timed diagnostics of heart disease allowed to perform operation in
the period of a newborn with good result and in short terms after operation to discharge from a hospital.
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About the authors
- Chvamaniya Aleksandr Aleksandrovich, Researcher;
- Svobodov Andrey Andreevich, Dr Med. Sc., Chief Researcher, Cardiac Surgeon, orcid.org/0000-0003-2523-5212;
- Kosheleva Lyudmila Vital'evna, Radiologist;
- Kotov Sergey Aleksandrovich, Cand. Med. Sc., Senior Researcher;
- Tumanyan Margarita Rollandovna, Dr Med. Sc., Professor, Head of Department, orcid.org/0000-0003-4250-8198
