Abstract
Heart’s benign tumors in children account for 90% all tumors heart and pericardium. Angiofibroma – tumor, consisting of fibrous tissue
with varying degrees of vascularity, characterized by cells proliferation around the blood vessels. After identifying tumors, surgeon
should determine whether it disorders hemodynamic, which will depend further tactics of treatment. If hemodynamic disorders are absence, patient should be followed up 1–2 times per year. If there is hemodynamic instability presence, necessary to determinate
possibility for tumor excision without basic heart structures damage. Tumor should be removed completely or even partially with
associate tissue radiofrequency ablation or cryotherapy. If haemodynamically significant tumor cannot be deleted it should be biopsied
with subsequent appointment for specialized treatment. Despite the fact that heart angiofibroma is histologically benign, clinical
manifestations often occurs acute hemodynamic instability and arrhythmia, which can lead to congestive heart failure. Angiofibroma
is most often localized in the right ventricle, right atrium and interventricular septum. In case of right atrium tumor location it’s possible
to radical resection and subsequent plastic wall atrium with a pericardial patch. In other cases palliative procedures are more common.
The article presents a case of successful removal of the angiofibroma of right atrium in a child first month of live.
References
Бокерия Л.А., Малашенков А.М., Kавсадзе В.Е., Серов Р.А.
Кардиоонкология. М.: НЦССХ им. А.Н. Бакулева; 2003:
175–206 / Bockeria L.A., Malashenkov A.M., Kavsadze V.E.,
Serov R.A. Cardiooncology. Moscow: A.N. Bakoulev
Scinetiffic Center for Cardiovascular Surgery; 2003: 175–206
(in Russ.).
Malipatil S.R. Extranasopharyngeal angiofibroma from nasal
vestibule: a rare presentation. Int. J. Otorhinolaryngol. Clin.
2013; 5 (3): 169–72.
Kim Y.Ju, Kim Y. Jin, Kim S.H., Park S. Primary cardiac
angiofbroma. Korean Circ. J. 2013; 43 (9): 636–9.
Beghetti M., Gow R.M., Haney I. et al. Pediatric primary benign
cardiac tumors: A 15-yers review. Am. Heart J. 1997; 134:
1107–14.
Culliford A., Levi R., Kronson I. The echocardiographic recognition
of an atrial myxoma vegetation. Am. Heart J. 1990;
119: 679–80.
Бокерия Л.А., Шаталов К.В. Детская кардиохирургия: Руководство для врачей. М.: НЦССХ им. А.Н. Бакулева; 2016:
851–9 / Bockeria L.A., Shatalov K.V. Children’s cardiosurgery:
Guide for physicians. Moscow: A.N. Bakoulev Scinetiffic
Center for Cardiovascular Surgery; 2016: 851–9 (in Russ.).
Ottaviani G., Rossi L., Ramos S.G., Matturi L. Pathology of the
heart and conduction system in a case of sudden death due to
a cardiac fibroma in a 6-month-old child. Cardiovasc. Pathol.
1999; 8: 109–12.
About the authors
- Kim Aleksey Ivanovich, Dr Med. Sc., Professor, Head of Department, orcid.org/0000-0002-1759-9895;
- Atmashkin Anton Anatol'evich, Postgraduate, Cardiovascular Surgeon, orcid.org/0000-0002-7894-9174;
- Erokhina Oksana Viktorovna, Cardiologist, orcid.org/0000-0002-7700-8823;
- Grigor'yants Tigran Rachikovich, Cand. Med. Sc., Senior Researcher, Cardiovascular Surgeon, orcid.org/0000-0001-9344-2593;
- Didyk Vadim Petrovich, Researcher, Cardiovascular Surgeon, orcid.org/0000-0002-8438-6339;
- Khugaev Georgiy Aleksandrovich, Junior Researcher, Pathologist
