Abstract
Objective. The purpose of this study was to investigate sensitivity, specificity and accuracy of the most known prognostic score systems in biventricular repair of different congenital heart diseases combined with left heart hypoplasia.
Material and methods. Retrospective analysis of 56 patients with different congenital heart diseases combined with left heart hypoplasia treated in the Bakoulev National Medical Research Center for Cardiovascular Surgery within the period from 2003 to 2015. Biventricular repair was performed to all the patients. Mitral valve Z-score at hospitalization in general group was –3.10±0.79 (from –0.86 to –4.70). Aortic valve Z-score –3.54±1.22 (ranged from –0.86 to –7.04). Left ventricular outflow tract Z-score was –3.21±1.04 (from –1.15 to –6.45). End-diastolic left ventricular volume was 19.53±3.98 (from 12 to 35) ml/m2. The following prognostic models were analyzed for each patient: Rhodes score, CHSS-1, Discriminant score, CHSS-2, 2V-score.
Results. Rhodes score: sensitivity 0.02; specificity 1; accuracy 0.16. CHSS-1: sensitivity 0.55; specificity 0.57; accuracy 0.55. Discriminant score: sensitivity 0.23; specificity 0.87; accuracy 0.32. CHSS-2: sensitivity 0.94; specificity 0.62; accuracy 0.89. 2V-score: sensitivity 0.67; specificity 0.38; accuracy 0.62. Early hospital mortality was 14.3% (8 patients).
Conclusion. Advantages, limitations and specificity of the most known prognostic score models were revealed in our investigation.
CHSS-2 и 2V-score are the most universal and accurate models for all ranges of congenital heart diseases combined with left heart
structures hypoplasia.
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About the authors
- Bakoulev National Medical Research Center for Cardiovascular Surgery of Ministry of Health of the Russian
-
Federation, Rublevskoe shosse, 135, Moscow, 121552, Russian Federation
