Abstract
Objective. To determine the ratios of total anomalous pulmonary venous connections (TAPVC) variants and to assess the risk factors of adverse cardiac events (death, frequency of postoperative complications and repeated interventions).
Materials and methods. In the reconstructive surgery department of the Bakulev Scientific Center 106 operations were performed on patients with TAPVC: 80 patients with isolated, and 26 in combination with complex congenital heart diseases (CHD). The average age at the time of surgery was 3.4±2.6 months (1 day – 11 months), body weight – 4.78±1.68 (2.72–9.46) kg. The diagnosis was confirmed by echocardiography. If there were diagnostic difficulties, CT scan with contrast or angiocardiography and catheterization were used. All surgeries were performed using cardiopulmonary bypass with moderate hypothermia and custodiol.
Results. Hospital mortality in the general group of patients was 13%. The maximum observation period was 13.3 years (160 places). Freedom from reinterventions in the general group of patients 1 year after surgery was 100%, in the five-year interval freedom from reintervention was 95.8%, in the ten-year interval 88.3%.
Conclusion. Each of the anatomical forms of TAPVC with different frequency of occurrence may be accompanied by obstruction of pulmonary veins, which has a decisive effect on the hemodynamic and disease clinical manifestations. Despite the improvement in the results of treatment, pulmonary venous stenosis after surgery remains one of the most important causes of immediate and longterm mortality.
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About the authors
- Anton A. Atmashkin, Junior Researcher, Cardiovascular Surgeon; ORCID
- Aleksey I. Kim, Dr. Med. Sci., Professor, Head of Department; ORCID
- Tigran R. Grigor'yants, Cand. Med. Sci., Senior Researcher, Cardiovascular Surgeon; ORCID
- Tat'yana V. Rogova, Dr. Med. Sci., Pediatric Cardiologist; ORCID
- Rasul M. Kurganov, Junior Researcher, Cardiovascular Surgeon; ORCID
- Aleksey E. Popov, Cand. Med. Sci., Researcher, Cardiovascular Surgeon; ORCID
