Abstract
Double aortic arch is the most common symptomatic vascular ring, accounting for 50–60% of vascular rings. Double aortic arch usually
presents between birth and 3 months, earlier than other symptomatic rings and with more severe symptoms. Occasionally, it can
be an incidental finding in older children and adults. There is no association with any major cardiac anomaly. Usually one arch is dominant
and the other arch is smaller or may be atretic. There are several types of double aortic arch. The right aortic arch amounts
0.1% of population. The left aortic arch with aberrant right subclavian artery is the most frequent aortic arch anomaly that amounts
0.5% of population. Cervical aortic arch is rare case with less than 0.01% of prevalence in which aortic arch located above clavicles
in cervical region. The management of this congenital disease is surgical. The surgical indications are presence of mediastinal visceral
compression symptoms with the vascular ring confirmed and presence of concomitant heart defects as well. Early and proper
surgical treatment is very important to avoid severe complications that can occur after hypoxic conditions and apnea.
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About the authors
- Sergey A. Kotov, Cand. Med. Sc., Senior Researcher, Cardiovascular Surgeon,
orcid.org/0000-0003-4570-4854;
- Andrey A. Svobodov, Dr. Med. Sc., Leading Researcher, Cardiovascular Surgeon,
orcid.org/0000-0003-2523-5212;
- Vadim S. Razumovskiy, Postgraduate, orcid.org/0000-0001-7802-4588;
- Nino T. Siria, Junior Researcher, Cardiologist, orcid.org/0000-0001-9594-6306
