Abstract
Success of surgical repair of congenital heart diseases depends on a number of factors. One of these factors is the concomitant pathology,
evaluation of which at the stage of operation planning allows to assess perioperative risk and develop measures to reduce the incidence
of complications. This report describes of successful repair of atrial septal defect in a small child with concomitant TAR syndrome. TAR
syndrome is extremely rare genetic disease, the main manifestations of which are thrombocytopenia and absence of radius bones.
Thrombocytopenia in this syndrome often leads to life-threatening bleeding, which is more relevant for children under 2 years of age. This
report describes the stages of the patient's examination, the choice of tactics for surgical treatment and management of the child in the
early postoperative period.
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About the authors
- Ivan T. Narmania, Postgraduate, Cardiovascular Surgeon, orcid.org/0000-0003-0936-6116;
- Dmitriy K. Gushchin, Researcher, Cardiovascular Surgeon, orcid.org/0000-0002-0925-6526;
- Aleksey A. Kupryashov, Senior Researcher, Dr Med. Sc., Head of Department, Cardiovascular Surgeon,
orcid.org/0000-0001-7673-4762
