Abstract
Primary cardiac tumors in infants are a rare pathology and occur in 0.03–0.32% of patients, in most cases (90%) tumors are benign. Among the registered congenital tumors, rhabdomyoma is most commonly diagnosed, fibroma is diagnosed less often. Cardiac fibroma does not regress, is clinically dangerous and can lead to complications: arrhythmia, embolism, respiratory and cardiac distress. The strategy for treating fibromas remains controversial – early surgery versus case follow-up. In case of hemodynamic disorders caused by space-occupying lesions, surgical treatment for tumor resection and maximum preservation of cardiac structures is justified for the patients. Fibroma develops from fibroblasts and myofibroblasts, which results in large losses of functional myocardium of the left ventricle (LV) and cardiac distress. One of the effective methods of treating this complication is extracorporeal membrane oxygenation (ECMO) both in pre- and post-surgery period. The presented clinical example illustrates a case of successful surgical treatment of hemodynamically significant LV fibroma in an infant followed by ECMO in the postoperative period. Assisted circulation for ten days contributed to the restoration of LV function.
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About the authors
- Ol’ga S. Yanulevich, Cand. Med. Sci., Pediatric Cardiologist; ORCID
- Roman S. Kozhanov, Resident; ORCID
- Оleg A. Egunov, Cardiovascular Surgeon; ORCID
- Aleksandr A. Sokolov, Dr. Med. Sci., Professor, Head of the Ultrasound and Functional
Diagnostics Laboratory; ORCID
- Evgeniy V. Krivoshchekov, Dr. Med. Sci., Cardiovascular Surgeon, Head of the Cardiovascular Surgery Department; ORCID
