Abstract
Fibroma is the second, after rhabdomyoma, most common benign tumor of the heart in children. We present the case report of a partial resection of a giant fibroma of the heart in a newborn, diagnosed prenatally. According to echocardiography, computed tomography (CT), magnetic resonance imaging of the heart, was identified a volume formation measuring 31× 36 × 38 mm, under the left atrioventricular junction, caused deformation of the LV chamber, narrowing of the left ventricle outflow tract (LVOT) (according to CT angiography narrowing to 4 mm) and dislocation of the subclavian structures of the mitral valve. The large volume of the tumor, as well as the intramural growth, excluded the possibility of complete safe removal of the tumor. After consulting with oncologists, it was decided to perform a resection of a part of the tumor in LVOT under cardiopulmonary bypass. The surgical material was taken for histological examination, according to the results of which the diagnosis was confirmed.
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About the authors
- Aleksey I. Kim, Dr. Med. Sci., Professor, Chief of Department of Cardiac Surgery of Newborns and Infants; ORCID
- Tat’yana V. Rogova, Dr. Med. Sci., Leading Researcher, Head of Department of Reconstructive Surgery of Newborns and Children of the First Year of the Life with Congenital Heart Defects, Cardiologist; ORCID
- Pyatimat R. Evloeva, Junior Researcher; ORCID
- Aleksey E. Popov, Cand. Med. Sci., Cardiovascular Surgeon; ORCID
- Ol’ga Yu. Dariy, Cand. Med. Sci., Radiologist; ORCID
- David R. Tevosov, Pathologist; ORCID
