Abstract
Isolated congenital atresia of the mouth of the left coronary artery is an extremely rare disease. This anomaly often leads to life-threatening complications, including sudden cardiac death, and therefore various types of surgical treatment are recommended. Due to the rare occurrence of pathology, only isolated cases of long-term outcomes of surgery are presented in the literature. A case of surgical treatment of atresia of the mouth of the left coronary artery, first identified in a child aged 6 years, is presented. The operation of mammarocoronary bypass surgery was performed. 1 year after the operation, ischemic changes were detected according to the treadmill test. On coronaroangiography a critical (95%) narrowing in the anastomosis area of the mammarocoronary shunt with a transition to the anterior descending artery was revealed. Transluminal balloon plastic surgery and mammarocoronary shunt stenting with the transition to the anterior descending artery were performed. 3 years after aorto-coronary bypass grafting (CABG) and 2 years after stenting, the patient was examined on an outpatient basis. The boy does not complain. According to echocardiography, there is no valvular pathology, the contractile function of the myocardium is preserved (left ventricular ejection fraction 69.4%). There were no ischemic changes on the ECG during the stress test.
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About the authors
- Mariya N. Nevedrova, Cand. Med. Sci., Researcher; ORCID
- Ol'ga I. Medvedeva, Dr. Med. Sci., Leading Researcher; ORCID
- Marina L. Ermolenko, Dr. Med. Sci., Chief of Department; ORCID
- Dmitriy V. Kovalev, Dr. Med. Sci., Leading Researcher; ORCID
- Elena A. Degtyareva, Dr. Med. Sci., Head of Hospital; ORCID
