Abstract
The choice of therapeutic approach newborns with an atresia of a pulmonary artery with the intact interventricular septum expressed by
a hypoplasia of the right heart with multiple sinusoids is based on a set of factors. In this case the option of stenting of an open arterial
duct 3 stents at the child of 2 days of life with the significant arterial hypoxaemia (42% saturation of capillary blood by oxygen) and symptoms
of an infection (omphalitis, leukocytosis is presented; procalcitonin 44 ng/ml at norm to 0.25). By results of echcardiogram fibrous
ring of the tricuspid valve of 6 mm (Z =–1.83), pulmonary valve of 3.8 mm (Z =–1.36). In the thickness of a myocardium of the right ventricle
extended sinusoids are located. Treatment within a day didn't lead to desirable result (SatO2 53.5%). To the child was perfomed of
stenting of open arterial duct, that allowed at the age of 17 days of life, in a satisfactory condition, with saturation of capillary blood by
oxygen of 75%, for therapies by digoxin and aspirin to transfer the child to department of pathology of newborns for preparation for the
following stage of surgical treatment. At the time of transfer diameter of a stream on a stenting arterial duct of 4 mm. End-diastolic volume
of 22 ml/sq.m. Multiple sinusoids. Readmissone is planned in 1 month of life.
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